Congenital Cystic Adenomatoid Malformation of the Lung

CONGENITAL CYSTIC ADENOMATOID malformation (CCAM) of the lung is a rare, multicystic lesion with embryonic origins. Approximately 421 cases have been documented since the lesion was first described in 1949.¹ Usually, only one lobe is affected, most often the lower lobe.² CCAM represents 25 percent of all congenital lung lesions.³ There is no race predominance, nor is there a left- or right-side trend.⁴ Males may be at greater risk than females for CCAM development.⁵