Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity
Crystal-storing histiocytosis is a rare immunoglobulin storage disorder most frequently associated with lymphoproliferative diseases and characterized by intracytoplasmic accumulations of fibrillar and crystalloid inclusions. The inclusions have been described in a variety of anatomic
sites but with only a few reported cases of CNS involvement. We presented 2 patients with cerebral crystal-storing histiocytosis and described the imaging characteristics that may distinguish brain parenchymal involvement by crystal-storing histiocytosis from other, more commonly encountered
mass lesions.
Keywords: CSH = crystal-storing histiocytosis
Document Type: Research Article
Publication date: 01 February 2019
This article was made available online on 18 December 2018 as a Fast Track article with title: "Multimodality Imaging of Cerebral Crystal-Storing Histiocytosis: Distinguishing Imaging Characteristics and a Literature Review of a Very Rare Entity".
- Neurographics is the peer-reviewed, quarterly educational journal of the American Society of Neuroradiology. The journal includes review articles as well as high-yield case reports that have been solicited from society meetings, including the annual meeting of the ASNR as well as the American Society of Spine Radiology, the American Society of Pediatric Neuroradiology, the American Society of Functional Neuroradiology, and the American Society of Head and Neck Radiology meetings. Unsolicited educational review articles and case reports are also accepted for review at the discretion of the Editor-in-Chief. Submissions focusing on a pictorial approach to educational objectives are highly encouraged. The journal is open access and available online. CME credit is offered for reading review articles and completing activity evaluations through the ASNR Education Connection website: https://www.pathlms.com/asnr
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