The successful use of recombinant factor VIIa in a patient with vascular-type Ehlers-Danlos syndrome

Authors: Faber; Craig¹; Duncan¹; Holliday²

Source: Acta Anaesthesiologica Scandinavica, Volume 51, Number 9, October 2007 , pp. 1277-1279(3)

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Abstract:

Vascular-type Ehlers-Danlos syndrome is an inherited connective tissue disorder resulting in an increased risk of serious peri-operative bleeding during surgery for spontaneous organ or vessel rupture. The excessive bleeding may result in coagulopathy, and thus compound the difficulty in securing surgical haemostasis. With the advent of recombinant factor VIIa, a new therapy has become available for the management of intractable surgical bleeding.

Keywords: Coagulopathy; Ehlers-Danlos syndrome vascular type; haemostasis; recombinant factor VIIa

Document Type: Research article

DOI: http://dx.doi.org/10.1111/j.1399-6576.2007.01416.x

Affiliations: 1: Departments of Surgery 2: Anaesthesia and Intensive Care, Raigmore Hospital, Inverness, UK

Publication date: 2007-10-01