Uncommon genetic syndromes and narrative production - Case Studies with Williams, Smith-Magenis and Prader-Willi Syndromes?
Authors: Garayzábal, Elena; Capó, Magdalena; Moruno, Esther; Gonçalves, Óscar F; Férnandez, Montserrat; Lens, MarÍa; Sampaio, Adriana
Source: International Journal of Developmental Disabilities, Volume 58, Number 1, March 2012 , pp. 48-65(18)
Publisher: Maney Publishing
This study compares narrative production among three syndromes with genetic microdeletions: Williams syndrome (WS), Smith-Magenis syndrome (SMS), and Prader-Willi syndrome (PWS), characterized by intellectual disabilities and relatively spared language abilities. Our objective is to study the quality of narrative production in the context of a common intellectual disability. To elicit a narrative production, the task Frog! Where Are You was used. Then, structure, process, and content of the narrative process were analysed in the three genetic disorders: WS (n = 2), SMS (n = 2), and PWS (n = 2).
Data show evidence of an overall low narrative quality in these syndromes, despite a high variability within different measures of narrative production.
Results support the hypothesis that narrative is a highly complex cognitive process and that, in a context of intellectual disability, there is no evidence of particular ‘hypernarrativity’ in these syndromes.
Document Type: Original Article
Publication date: 2012-03-01
- In 2012 the British Journal of Developmental Disabilities changed its name to International Journal of Developmental Disabilities to reflect its international authorship, subject matter and subscriber base. View the issues of British Journal of Developmental Disabilities available online.
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