Cystic meningioangiomatosis in neurofibromatosis type 2: an MRI-pathological study

Authors: FEDI, M; KALNINS, R M; SHUEY, N; FITT, G J; NEWTON, M; MITCHELL, L A

Source: British Journal of Radiology, Volume 82, Number 979, July 2009 , pp. e129-e132(4)

Publisher: British Institute of Radiology

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Abstract:

We report cerebral cystic meningioangiomatosis in a patient with neurofibromatosis type 2. An 18-year-old woman presented with progressive hemiparesis secondary to a meningioma at the foramen magnum. Her MR examination also demonstrated three small cortical and subcortical cystic lesions. She underwent surgery for the meningioma, but died from brainstem infarction. Post-mortem histopathological examination of the cystic lesions showed enlarged subcortical perivascular spaces with overlying meningioangiomatosis. The unusual features and possible pathogenesis are discussed.

Document Type: Case report

DOI: http://dx.doi.org/10.1259/bjr/56536580

Publication date: 2009-07-01