IngentaConnect Intraoral Findings of Papillon-LeFevre Syndrome

Authors: Canger, Emin Murat¹; Celenk, Peruze¹; Devrim, Inci²; Yenisey, Murat³; Gunhan, Omer⁴

Source: Journal of Dentistry for Children, Volume 75, Number 1, January-April 2008 , pp. 99-103(5)

Publisher: American Academy of Pediatric Dentistry

Abstract:

Papillon-Lefevre syndrome (PLS) is a rare autosomal, recessive condition characterized by hyperkeratosis of palms and soles of the feet and elbows and by rapid formation of periodontitis and hypermobility, migration and exfoliation of the teeth of primary and permanent dentition. The purpose of this report was to describe the case of an 8-year-old boy who presented to the Department of Oral Diagnosis and Radiology of Faculty of Dentistry of Ondokuz Mayis University with a chief complaint of mobility and rapid loss of teeth. Hyperkeratosis of palms and soles were realized. His gingivae were hyperemic and edematous, and the teeth were mobile. Histopathological examination of the specimen taken from the thickened skin was reported to be consistent with PLS. All teeth with poor prognosis were extracted and extensive periodontal therapy was administered, and a special denture was constructed.

Keywords: PAPILLON-LEFEVRE SYNDROME; PALMOPLANTAR HYPERKERATOSIS; PREMATURE TOOTH LOSS; PERIODONTAL DESTRUCTION

Document Type: Case report

Affiliations: 1: Department of Oral Diagnosis and Radiology, Faculty of Dentistry, Ondokuz Mayis University, Samsun, Turkey 2: Department of Periodontology, Faculty of Dentistry, Ondokuz Mayis University, Samsun, Turkey 3: Department of Prosthodontics, Faculty of Dentistry, Ondokuz Mayis University, Samsun, Turkey 4: Department of Pathology, Gulhane Military Academy of Medicine, Ankara, Turkey

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